The role of pediatric dentists in managing the oral needs of patients with Cleidocranial Dysplasia
The role of pediatric dentists in managing the oral needs of patients with Cleidocranial Dysplasia
DOI:
https://doi.org/10.51473/rcmos.v1i2.2025.1716Keywords:
Cleidocranial Dysplasia, Pediatric Dentistry, Dental Anomalies, Dental Management, Children's Oral Health.Abstract
Introduction: Cleidocranial dysplasia (CCD) is a rare congenital skeletal condition with auto-somal dominant inheritance and wide clinical variability. The prevalence is estimated at 1:1,000,000, with no gender predilection and no impact on cognitive abilities. Objective: This study aims to analyze the role of pediatric dentists in the management of CCD in children, a genetic condition that affects craniodentofacial formation and causes functional and aesthetic changes. Materials and Methods: This is a narrative review based on articles available in the PubMed database. Studies on CCD in pediatric patients were included, focusing on etiopa-thogenesis and clinical reports relevant to dental management. There was no temporal delimi-tation. Literature Review: The diagnosis of CCD is made through the analysis of clinical and radiographic signs, usually visible since childhood. Prolonged retention of deciduous teeth, delayed eruption of permanent teeth, and supernumerary teeth are common. Pediatric dentists are often the first to identify such signs, favoring early diagnosis and effective therapeutic strategies. Final Considerations: Pediatric dentists play a central role in the diagnosis and mo-nitoring of CHD, working in a multidisciplinary manner to promote oral health and quality of life. Although there have been advances, there are still gaps in the literature, reinforcing the need for more research and specific clinical protocols for the care of these patients.
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